口腔医学研究 ›› 2016, Vol. 32 ›› Issue (9): 992-993.DOI: 10.13701/j.cnki.kqyxyj.2016.09.025

• 病例报告 • 上一篇    下一篇

遗传性乳恒牙牙本质发育异常1例——附临床调查及病理学研究

徐山山1,于彦君1,刘麒麟2,胡荣荣1,孙宏晨3,陈远萍1*   

  1. 1. 吉林大学口腔医学院正畸科 吉林 长春 130021;
    2. 吉林大学口腔医学院口腔颌面外科;
    3. 吉林省牙发育及颌骨重塑与再生重点实验室
  • 收稿日期:2016-03-07 出版日期:2016-09-26 发布日期:2016-09-26
  • 通讯作者: 陈远萍,E-mail:chenyuanping1962@sina.com
  • 作者简介:徐山山(1988~ ),女,山东省日照市人,硕士在读,主要从事口腔正畸的临床治疗工作。

Case Report: Clinical Investigation and Pathology on a Case of Hereditary Dentine Dysplasia of Deciduous and Permanent Teeth

XU Shan-shan1, YU Yan-jun1, LIU Qi-lin2, HU Rong-rong 1, SUN Hong-chen3, CHEN Yuan-ping1*   

  1. 1. Department of Orthodontics, School and Hospital of Stomatology, Jilin University, Changchun 130021, China;
    2. Department of Oral and Maxillofacial Surgery, School and Hospital of Stomatology, Jilin University, Changchun 130021, China;
    3. Jilin Provincial Key Laboratory of Tooth Development and Bone Remodeling. Changchun 130021, China.
  • Received:2016-03-07 Online:2016-09-26 Published:2016-09-26

摘要: 牙本质发育不良I型(dentin dysplasia type Ⅰ,DD-Ⅰ)是一种十分罕见的牙本质发育异常的常染色体显性遗传疾病。本文报告1例乳恒牙牙本质发育异常的病例.通过对该患者进行相关临床检查,影像学检查及组织病理学检查明确诊断,进一步通过定期随访观察其恒牙萌替变化,并结合相关文献进行讨论,为此病的进一步研究补充资料。

关键词: 牙本质发育不良I型, 髓腔闭锁, 牙根短

Abstract: Dentin dysplasia type I (DD-I) is a very rare autosomal dominant disease which exhibits dentine abnormal development. This paper reports a case of dentin dysplasia of primary and permanent teeth. The diagnosis was confirmed through the clinical, imaging and histopathological examinations, the changes in permanent teeth eruption were observed by regular follow-up, and the discussion was performed with combined the related literature. All of these provided data for further studies on this disease.

Key words: Dentin dysplasia type I, Dedullary cavity, Short root

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